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HERO ID
571383
Reference Type
Journal Article
Title
Early repolarization syndrome: Is it always benign?
Author(s)
Letsas, KP; Efremidis, M; Pappas, LK; Gavrielatos, G; Markou, V; Sideris, A; Kardaras, F
Year
2007
Is Peer Reviewed?
Yes
Journal
International Journal of Cardiology
ISSN:
0167-5273
EISSN:
1874-1754
Volume
114
Issue
3
Page Numbers
390-392
DOI
10.1016/j.ijcard.2005.11.078
Abstract
Early repolarization syndrome is a well-recognized idiopathic electrocardiographic phenomenon characterized by prominent J wave and ST-segment elevation predominantly in left precordial leads. The syndrome shares remarkable cellular, ionic, and electrocardiographic similarities with the Brugada syndrome and idiopathic ventricular fibrillation (a variant of the Brugada sydrome with ST-segment elevation in inferior leads). Although early repolarization syndrome is considered a benign entity, its arrhythmogenic potential still remains unknown. We report the case of a 39-year-old male with a family history of sudden death and an electrocardiogram consistent with early repolarization syndrome. Diagnostic dilemmas are discussed.
Keywords
Early repolarization syndrome; Brugada syndrome; Idiopathic ventricular fibrillation; Sudden death
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