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7108630 
Journal Article 
Friedreich's ataxia. A neurocardiac disease 
Reinhardt, F; Erbguth, F; Reynen, K; Claus, D; Neundorfer, B; , 
1997 
Yes 
Der Nervenarzt
ISSN: 0028-2804
EISSN: 1433-0407 
SPRINGER VERLAG 
NEW YORK 
678-681 
9380217 
WOS:A1997XV28500013 
Friedreich's ataxia (FA) represents a degenerative, genetically determined disease of the nervous system in combination with myocardial affection and in some cases endocrinological disturbances. Manifestation of myocardial involvement usually follows symptoms of nervous system degeneration later in the course, but seems not to be secondary. These cardiac disturbances are the main cause of death in FA-patients. Therapeutic management of heart disease is possible and interdisciplinary neurologic-cardiologic cooperation should start early in the course of FA.