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7136513 
Journal Article 
Brachial Amyotrophic Diplegia: Case Report 
Yucel, M; Oz, O; Akgun, H; Korkmaz, M; Ulas, UH; Demirkaya, S; Kutukcu, Y; Odabasi, Z; , 
2011 
Yes 
Journal of Neurological Sciences (Print)
ISSN: 1302-1664 
JOURNAL NEUROLOGICAL SCIENCES 
BORNOVA-IZMIR 
86-90 
WOS:000288679800012 
Two forms of Amyotrophic lateral sclerosis (ALS) subtypes have been recognized since the late 19th and early 20th centuries but relatively inadequately studied, these being the flail arm (FA) and flail leg (FL) syndromes. The FA phenotype was described by Vulpian in 1886 as a syndrome of proximal weakness and wasting of the upper limbs (scapulohumeral variant of progressive muscular atrophy or forme scapulo-hume' rale). The condition has been variously termed as Vulpian-Bernhardt syndrome, hanging-arm syndrome, neurogenic man-in-a-barrel syndrome, brachial amyotrophic diplegia, or the FA syndrome. The syndrome typically presents with progressive upper limb weakness and wasting that is often symmetric and proximal, without significant functional involvement of lower limbs or bulbar muscles. Here we presented a patient with complaints of difficulty in lifting his right arm in his medical history. Brachial amyotrophic diplegia was diagnosed with neurological examination and EMG findings. It is presented because of rarity.